Last reviewed · How we verify

NCT05514873

An Open-label Study to Evaluate the Safety, Tolerability, and Efficacy of Subcutaneous Zilucoplan in Participants With Generalized Myasthenia Gravis Who Were Previously Receiving Intravenous Complement Component 5 Inhibitors

Completed Phase 3 Results posted Last updated 3 September 2025
What this trial tests

Phase 3 trial testing zilucoplan (RA101495) in Generalized Myasthenia Gravis in 26 participants. Completed in 23 October 2024.

Timeline
31 October 2022
Primary endpoint
13 March 2024
23 October 2024

Quick facts

Lead sponsorUCB Biopharma SRL
PhasePhase 3
StatusCompleted
Study typeINTERVENTIONAL
Allocationna
Designsingle group
Maskingnone
Primary purposetreatment
Enrollment26
Start date31 October 2022
Primary completion13 March 2024
Estimated completion23 October 2024
Sites12 locations across United States

Drugs / interventions tested

Conditions studied

Sponsor

UCB Biopharma SRL — full company profile →

Who can join

Adults 18 to 85, any sex, with Generalized Myasthenia Gravis. Patients with the condition only — healthy volunteers not accepted.

Results — posted to ClinicalTrials.gov

Per-arm endpoint measurements with 95% confidence intervals where reported. Source: trial results section.

Percentage of Participants With Treatment-emergent Adverse Events (TEAEs) Over the Main Treatment Period Primary · From Baseline (Day 1) to Safety Follow-Up Visit (40 days post last dose) of Main Treatment Period (up to approximately 19 weeks)

An AE was any untoward medical occurrence in a patient or clinical study participant, temporally associated with the use of study medication, whether or not considered related to the study medication. A TEAE was defined as an AE starting on or after the time of first administration of investigational medicinal product (IMP) and up to and including 40 days after the final dose (or last contact depending on which occurs first).

GroupValue95% CI
Zilucoplan 0.3 mg/kg73.1
Percentage of Participants With TEAEs Leading to Withdrawal of Study Medication Over the Main Treatment Period Primary · From Baseline (Day 1) to Safety Follow-Up Visit (40 days post last dose) of Main Treatment Period (up to approximately 19 weeks)

An AE was any untoward medical occurrence in a patient or clinical study participant, temporally associated with the use of study medication, whether or not considered related to the study medication. A TEAE was defined as an AE starting on or after the time of first administration of IMP and up to and including 40 days after the final dose (or last contact depending on which occurs first).

GroupValue95% CI
Zilucoplan 0.3 mg/kg7.7
Change From Baseline to Week 12 in Myasthenia Gravis-Activities of Daily Living (MG-ADL) Score Secondary · From Baseline to Week 12

The MG-ADL is a brief 8-item interviewer-administered patient-reported outcome (PRO) designed to evaluate MG symptom severity. The MG-ADL targets symptoms and disability across ocular, bulbar, respiratory, and axial symptoms. Each item is assessed on a 4-point scale, where a score of 0 represents normal function and a score of 3 represents severely decreased ability to perform that function. The total MG-ADL score ranges from 0 to 24, with a higher score indicating more severe impairment. A positive change in score indicates worsening and negative change indicates improvement.

GroupValue95% CI
Zilucoplan 0.3 mg/kg-1.15-2.11 – -0.19
Change From Baseline to Week 12 in the Quantitative Myasthenia Gravis (QMG) Score Secondary · From Baseline to Week 12

The QMG is a standardized and validated quantitative strength scoring system that included 13 items in the following categories: ocular and facial involvement, swallowing, speech, limb strength, and forced vital capacity. Scoring for each item ranges from no weakness (0) to severe weakness (3), with an overall score range from 0 to 39. Higher scores represent more severe impairment. A positive change in score indicates worsening and negative change indicates improvement.

GroupValue95% CI
Zilucoplan 0.3 mg/kg-1.24-2.64 – 0.16
Percentage of Participants With Serious TEAEs Over the Main Treatment Period Secondary · From Baseline (Day 1) to Safety Follow-Up Visit (40 days post last dose) of Main Treatment Period (up to approximately 19 weeks)

Treatment-emergent serious adverse events (serious TEAEs) were any untoward medical incidence in a participant during administered study treatment, whether or not these events were related to study treatment and additionally were emergent untoward medical occurrence that at any dose: * Results in death * Is life-threatening * Required in patient hospitalisation or prolongation of existing hospitalisation * Results in persistent disability/incapacity * Was a congenital anomaly or birth defect * Important medical events

GroupValue95% CI
Zilucoplan 0.3 mg/kg3.8
Percentage of Participants With Study Withdrawal Over the Main Treatment Period Secondary · From Baseline (Day 1) to Safety Follow-Up Visit (40 days post last dose) of Main Treatment Period (up to approximately 19 weeks)

Percentage of participants with study withdrawal based to pre-defined reasons in the protocol were reported.

GroupValue95% CI
Zilucoplan 0.3 mg/kg11.5

Adverse events — posted to ClinicalTrials.gov

Time frame: From Baseline up to 84 weeks (Overall Treatment Period). Reporting threshold: 5%. Adverse-event reports describe events observed during the trial — not all are caused by the drug.

Zilucoplan 0.3 mg/kg (Overall Treatment Period)
Serious: 5/26 (19%)
Deaths: 0/26

Serious adverse events (9 terms)

ReactionSystemZilucoplan 0.3 mg/kg (Over…
Myasthenia gravisNervous system disorders
DiverticulitisInfections and infestations
COVID-19Infections and infestations
PyelonephritisInfections and infestations
Metapneumovirus infectionInfections and infestations
HyperglycaemiaMetabolism and nutrition disorders
Lactic acidosisMetabolism and nutrition disorders
DyspnoeaRespiratory, thoracic and mediastinal disorders
HypoxiaRespiratory, thoracic and mediastinal disorders
Other adverse events (17 terms — click to expand)

ReactionSystemZilucoplan 0.3 mg/kg (Over…
Amylase increasedInvestigations
Lipase increasedInvestigations
COVID-19Infections and infestations
DiarrhoeaGastrointestinal disorders
NauseaGastrointestinal disorders
Myasthenia gravisNervous system disorders
PainGeneral disorders
Injection site painGeneral disorders
SinusitisInfections and infestations
Injection site bruisingGeneral disorders
Injection site pruritusGeneral disorders
Herpes zosterInfections and infestations
NasopharyngitisInfections and infestations
ArthralgiaMusculoskeletal and connective tissue disorders
Back painMusculoskeletal and connective tissue disorders
CoughRespiratory, thoracic and mediastinal disorders
RashSkin and subcutaneous tissue disorders

Most-reported serious reactions: Myasthenia gravis, Diverticulitis, COVID-19, Pyelonephritis, Metapneumovirus infection, Hyperglycaemia, Lactic acidosis, Dyspnoea.

Data from ClinicalTrials.gov NCT05514873 adverse events section.

Sponsor's own description

The purpose of the study is to evaluate the safety and tolerability of switching from intravenous (IV) complement component 5 (C5) inhibitors to subcutaneous (SC) Zilucoplan in study participants with generalized myasthenia gravis (gMG)

Publications & conference data

4 peer-reviewed publications reference this trial (live from Europe PMC):

  1. Zilucoplan: First Approval.
    Shirley M. · · 2024 · cited 21× · PMID 38093160 · DOI 10.1007/s40265-023-01977-3
  2. Nanodrug Delivery Systems for Myasthenia Gravis: Advances and Perspectives.
    Huang J, Yan Z, Song Y, Chen T. · · 2024 · cited 7× · PMID 38794313 · DOI 10.3390/pharmaceutics16050651
  3. The role of complement in the immunopathogenesis of acetylcholine receptor antibody-positive generalized myasthenia gravis: bystander or key player?
    Michailidou I, Patsiarika A, Kesidou E, Boziki MK, et al · · 2025 · cited 2× · PMID 40303417 · DOI 10.3389/fimmu.2025.1526317
  4. Switching to subcutaneous zilucoplan from intravenous complement component 5 inhibitors in generalised myasthenia gravis: a phase IIIb, open-label study.
    Freimer M, Desai U, Govindarajan R, Kang MK, et al · · 2025 · cited 1× · PMID 40620733 · DOI 10.1177/17562864251347283

Verify or expand the search:

Other trials of zilucoplan (RA101495)

Trials testing the same drug.

Other recruiting trials for Generalized Myasthenia Gravis

Currently open trials in the same condition.

Other UCB Biopharma SRL trials

Trials by the same sponsor.

Verify against primary sources

Data sources for this page

Drug Landscape aggregates and links these public records for informational use only. Always verify against the primary source before clinical or regulatory decisions. Canonical URL: https://druglandscape.com/trial/NCT05514873.

Primary sources · FDA · ClinicalTrials.gov · EMA · SEC EDGAR · ChEMBL · Wikidata · full sourcing