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Vyondys 53 (GOLODIRSEN)
Vyondys 53 works by binding to specific RNA sequences to prevent the production of a faulty dystrophin protein.
Vyondys 53 (golodirsen) is an antisense oligonucleotide developed by Sarepta Therapeutics, targeting exon 53 of dystrophin pre-mRNA to treat Duchenne muscular dystrophy. It was FDA-approved in 2019 and remains a patented product with no generic manufacturers. Vyondys 53 works by binding to specific RNA sequences, preventing the production of a faulty dystrophin protein. Key safety considerations include its short half-life of 3.4 hours, and the potential for liver enzyme elevations. As a patented product, its commercial status is secure.
At a glance
| Generic name | GOLODIRSEN |
|---|---|
| Sponsor | Sarepta |
| Drug class | Antisense Oligonucleotide [EPC] |
| Target | exon 53 of dystrophin pre-mRNA |
| Modality | Oligonucleotide |
| Therapeutic area | Rare Disease |
| Phase | FDA-approved |
| First approval | 2019 |
| Annual revenue | 400 |
Mechanism of action
Golodirsen is designed to bind to exon 53 of dystrophin pre-mRNA resulting in exclusion of this exon during mRNA processing in patients with genetic mutations that are amenable to exon 53 skipping. Exon 53 skipping is intended to allow for production of an internally truncated dystrophin protein in patients with genetic mutations that are amenable to exon 53 skipping [see Clinical Studies (14)].
Approved indications
- Duchenne muscular dystrophy
Common side effects
- Headache
- Pyrexia
- Fall
- Abdominal pain
- Nasopharyngitis
- Cough
- Vomiting
- Nausea
- Administration site pain
- Back pain
- Diarrhea
- Dizziness
Key clinical trials
- Study of SRP-4045 (Casimersen) and SRP-4053 (Golodirsen) in Participants With Duchenne Muscular Dystrophy (DMD) (PHASE3)
- A Long-term Observational Study Evaluating Eteplirsen, Golodirsen, or Casimersen in Routine Clinical Practice
- An Extension Study to Evaluate Casimersen or Golodirsen in Patients With Duchenne Muscular Dystrophy (PHASE3)
- A 48-Week, Open Label, Study to Evaluate the Efficacy and Safety of AMONDYS 45, EXONDYS 51, VYONDYS 53 in Subjects With DuchenneMuscular Dystrophy Carrying Eligible DMD Duplications. (PHASE2)
- An Open-Label Study of Golodirsen in Non-Ambulant Patients With Duchenne Muscular Dystrophy (PHASE4)
- Phase I/II Study of SRP-4053 in DMD Patients (PHASE1,PHASE2)
Patents
| Patent | Expiry | Type |
|---|---|---|
Primary sources
Every claim on this page is sourced from regulatory or scientific primary sources. See our editorial policy for full methodology.
| Source | Used for |
|---|---|
| FDA label | Mechanism, indications, dosing, boxed warnings, drug interactions |
| ClinicalTrials.gov | Trial enrolment, design, endpoints, results |
| FDA Orange Book | Patents + exclusivity |
| SEC EDGAR | Revenue + earnings |