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CINRYZE 1000 U

Shire · Phase 3 active Small molecule

CINRYZE is a C1 esterase inhibitor (C1-INH) that replaces or augments deficient or dysfunctional C1 inhibitor protein to prevent excessive bradykinin generation and control hereditary angioedema attacks.

CINRYZE is a C1 esterase inhibitor (C1-INH) that replaces or augments deficient or dysfunctional C1 inhibitor protein to prevent excessive bradykinin generation and control hereditary angioedema attacks. Used for Hereditary angioedema (HAE) Types I and II — acute attack treatment and prophylaxis.

At a glance

Generic nameCINRYZE 1000 U
SponsorShire
Drug classC1 esterase inhibitor (C1-INH) replacement therapy
TargetC1 esterase inhibitor (C1-INH); contact system cascade (Factor XII, kallikrein pathway)
ModalitySmall molecule
Therapeutic areaImmunology / Rare Genetic Disorders
PhasePhase 3

Mechanism of action

Hereditary angioedema (HAE) results from deficiency or dysfunction of C1 esterase inhibitor, a regulatory protein in the contact system cascade. Without adequate C1-INH, uncontrolled activation of Factor XII and kallikrein leads to excessive bradykinin production, causing severe angioedema. CINRYZE provides exogenous C1-INH to restore normal regulation of this cascade and prevent or reduce the frequency and severity of angioedema attacks.

Approved indications

Common side effects

Key clinical trials

Primary sources

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SourceUsed for
ClinicalTrials.govTrial enrolment, design, endpoints, results

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