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Acoramidis (AG10)

Eidos Therapeutics, a BridgeBio company · Phase 3 active Small molecule Under review Quality 0/100

Acoramidis (AG10) is a Transthyretin stabilizer Small molecule drug developed by Eidos Therapeutics, a BridgeBio company. It is currently in Phase 3 development for Transthyretin amyloid cardiomyopathy (ATTR-CM), Hereditary transthyretin amyloidosis (hATTR). Also known as: ALXN2060, AG10, ALXN 2060.

Acoramidis stabilizes transthyretin (TTR) protein to prevent its misfolding and aggregation, which causes amyloid disease.

Acoramidis (AG10) is a small molecule drug that stabilizes transthyretin, a protein associated with amyloidosis. It is being studied for the treatment of conditions such as amyloid cardiomyopathy and familial amyloidosis.

Likelihood of approval
63.3% vs 58.3% industry baseline
If approved by FDA: likely 2028–2030
Steps remaining: NDA/BLA submission
Confidence: High
Why this estimate
  • Baseline phase 3 → approval rate +58.3pp
    Industry-wide phase 3 drugs reach approval ~58.3% of the time (BIO/Informa 2023 industry benchmark across all therapeutic areas).
  • Rare-disease pathway favourability +5.0pp
    Rare-disease drugs benefit from FDA Orphan Drug Act, smaller pivotal trials, and more flexible endpoints. Approval rates run ~5pp above baseline.
Predicted approval windows by jurisdiction (conditional on FDA approval)
Regulator Country Likely year Lag vs FDA
FDA US 2028–2030
EMA EU 2029–2031 +0.7 yr
MHRA GB 2029–2031 +0.7 yr
Health Canada CA 2029–2032 +0.9 yr
TGA AU 2029–2032 +1.2 yr
PMDA JP 2029–2032 +1.5 yr
NMPA CN 2030–2033 +2.3 yr
MFDS KR 2029–2032 +1.4 yr
CDSCO IN 2029–2033 +1.8 yr
ANVISA BR 2030–2033 +2.3 yr

Hover any row for the lag rationale. Lag estimates are reduced when the drug has FDA Breakthrough or EMA PRIME designation (sponsors file globally in parallel).

Estimate based on the BIO/Informa industry phase transition rates plus per-drug modifiers for therapeutic area, sponsor type, FDA designations, mechanism, and trial design. Per-jurisdiction lags from Tufts CSDD international approval studies. Not investment, clinical or regulatory advice. Methodology: /methodology#likelihood.

At a glance

Generic nameAcoramidis (AG10)
Also known asALXN2060, AG10, ALXN 2060
SponsorEidos Therapeutics, a BridgeBio company
Drug classTransthyretin stabilizer
TargetTransthyretin (TTR)
ModalitySmall molecule
Therapeutic areaRare disease / Cardiology
PhasePhase 3

Mechanism of action

Acoramidis is a selective transthyretin stabilizer that binds to the TTR protein and increases its thermodynamic stability, preventing dissociation and subsequent misfolding into amyloid fibrils. By stabilizing the native TTR tetramer, the drug reduces amyloid formation and deposition in tissues, thereby slowing or halting disease progression in transthyretin amyloidosis.

Approved indications

Common side effects

Key clinical trials

Primary sources

Every claim on this page is sourced from regulatory or scientific primary sources. See our editorial policy for full methodology.

SourceUsed for
ClinicalTrials.govTrial enrolment, design, endpoints, results

Competitive intelligence

For the full competitive landscape — auto-detected comparators, recent regulatory actions across the set, upcoming PDUFA, patent timeline, sponsor landscape:

Frequently asked questions about Acoramidis (AG10)

What is Acoramidis (AG10)?

Acoramidis (AG10) is a Transthyretin stabilizer drug developed by Eidos Therapeutics, a BridgeBio company, indicated for Transthyretin amyloid cardiomyopathy (ATTR-CM), Hereditary transthyretin amyloidosis (hATTR).

How does Acoramidis (AG10) work?

Acoramidis stabilizes transthyretin (TTR) protein to prevent its misfolding and aggregation, which causes amyloid disease.

What is Acoramidis (AG10) used for?

Acoramidis (AG10) is indicated for Transthyretin amyloid cardiomyopathy (ATTR-CM), Hereditary transthyretin amyloidosis (hATTR).

Who makes Acoramidis (AG10)?

Acoramidis (AG10) is developed by Eidos Therapeutics, a BridgeBio company (see full Eidos Therapeutics, a BridgeBio company pipeline at /company/eidos-therapeutics-a-bridgebio-company).

Is Acoramidis (AG10) also known as anything else?

Acoramidis (AG10) is also known as ALXN2060, AG10, ALXN 2060.

What drug class is Acoramidis (AG10) in?

Acoramidis (AG10) belongs to the Transthyretin stabilizer class. See all Transthyretin stabilizer drugs at /class/transthyretin-stabilizer.

What development phase is Acoramidis (AG10) in?

Acoramidis (AG10) is in Phase 3.

What are the side effects of Acoramidis (AG10)?

Common side effects of Acoramidis (AG10) include Peripheral edema, Dyspnea, Fatigue, Diarrhea.

What does Acoramidis (AG10) target?

Acoramidis (AG10) targets Transthyretin (TTR) and is a Transthyretin stabilizer.

Related

Primary sources · FDA · ClinicalTrials.gov · EMA · SEC EDGAR · ChEMBL · Wikidata · full sourcing