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N-Acetylleucine (ACETYLLEUCINE)

Phase 2 active Small molecule ✓ Verified Jun 2026

N-Acetylleucine (generic name: ACETYLLEUCINE) is a acetylleucine drug. It is currently in Phase 2 development.

N-Acetylleucine works by inhibiting the enzyme leucine aminopeptidase, which breaks down certain amino acids.

N-Acetylleucine, also known as N-Acetyl-L-Leucine, is being studied as a potential treatment for several rare genetic disorders, including Ataxia-Telangiectasia, Niemann-Pick Disease, Type C, and GM2 Gangliosidosis. A pivotal study, IB1001-303, is currently investigating the effects of N-Acetyl-L-Leucine on Ataxia-Telangiectasia in a Phase III, randomized, placebo-controlled, double-blind, crossover study.

Likelihood of approval
15.3% vs 15.3% industry baseline
If approved by FDA: likely 2031–2034
Steps remaining: Phase 3 → NDA/BLA submission
Confidence: Medium
Why this estimate
  • Baseline phase 2 → approval rate +15.3pp
    Industry-wide phase 2 drugs reach approval ~15.3% of the time (BIO/Informa 2023 industry benchmark across all therapeutic areas).
Predicted approval windows by jurisdiction (conditional on FDA approval)
Regulator Country Likely year Lag vs FDA
FDA US 2031–2034
EMA EU 2032–2035 +0.7 yr
MHRA GB 2032–2035 +0.7 yr
Health Canada CA 2032–2036 +0.9 yr
TGA AU 2032–2036 +1.2 yr
PMDA JP 2032–2036 +1.5 yr
NMPA CN 2033–2037 +2.3 yr
MFDS KR 2032–2036 +1.4 yr
CDSCO IN 2032–2037 +1.8 yr
ANVISA BR 2033–2037 +2.3 yr

Hover any row for the lag rationale. Lag estimates are reduced when the drug has FDA Breakthrough or EMA PRIME designation (sponsors file globally in parallel).

Estimate based on the BIO/Informa industry phase transition rates plus per-drug modifiers for therapeutic area, sponsor type, FDA designations, mechanism, and trial design. Per-jurisdiction lags from Tufts CSDD international approval studies. Not investment, clinical or regulatory advice. Methodology: /methodology#likelihood.

At a glance

Generic nameACETYLLEUCINE
Drug classacetylleucine
ModalitySmall molecule
Therapeutic areaOther
PhasePhase 2

Mechanism of action

Think of it like a traffic cop: N-Acetylleucine helps direct the flow of amino acids in the body by blocking the enzyme that breaks them down. This can help increase the levels of these amino acids, which are important for various bodily functions. By doing so, it may help alleviate certain conditions, although its exact effects are still unknown.

Approved indications

No approved indications tracked.

Common side effects

Key clinical trials

Primary sources

Every claim on this page is sourced from regulatory or scientific primary sources. See our editorial policy for full methodology.

SourceUsed for
ClinicalTrials.govTrial enrolment, design, endpoints, results

Competitive intelligence

For the full competitive landscape — auto-detected comparators, recent regulatory actions across the set, upcoming PDUFA, patent timeline, sponsor landscape:

Frequently asked questions about N-Acetylleucine

What is N-Acetylleucine?

N-Acetylleucine (ACETYLLEUCINE) is a acetylleucine drug.

How does N-Acetylleucine work?

N-Acetylleucine works by inhibiting the enzyme leucine aminopeptidase, which breaks down certain amino acids.

What is the generic name of N-Acetylleucine?

ACETYLLEUCINE is the generic (nonproprietary) name of N-Acetylleucine.

What drug class is N-Acetylleucine in?

N-Acetylleucine belongs to the acetylleucine class. See all acetylleucine drugs at /class/acetylleucine.

What development phase is N-Acetylleucine in?

N-Acetylleucine is in Phase 2.

What are the side effects of N-Acetylleucine?

Common side effects of N-Acetylleucine include Hepatitis acute, Anticoagulation drug level above therapeutic, Haematoma, Inappropriate antidiuretic hormone secretion.

Related

Primary sources · FDA · ClinicalTrials.gov · EMA · SEC EDGAR · ChEMBL · Wikidata · full sourcing